ʻAno o ka ʻatikala
maʻi maʻi anemiahe ʻano o ka maʻi maʻi sickle cell. Hoʻopilikia ia i nā ʻāpana koko ʻulaʻula a me kahi protein i kapa ʻia he hemoglobin. No ka mea, he hoʻoilina, ʻē aʻe anemia ʻano like ʻole. No ka mea, he genetic ia a hoʻoili ʻia mai nā mākua i kā lākou mau keiki.
I kēia manawa ka mālama ʻana i ka maʻi maʻi maʻi anemia ʻaʻohe. Aia nā koho lapaʻau e mālama i nā hōʻailona a hōʻemi i nā pilikia.
nā maʻi maʻi maʻi maʻi maʻi maʻi anemiaʻO kahi hapa nui o ka hao, zinc, keleawe, ʻakika folic, pyridoxine, vitamina D a me Vitamin E e like me ka hemahema o ka meaʻai.
ʻAi kaulike; e like me ka lohi o ka ulu ʻana a me ka hoʻomohala ʻana, ka emi ʻana o ka iwi iwi, ka piʻi ʻana o ka haʻihaʻi, nā pilikia o ka ʻike, hiki i nā maʻi. maʻi maʻi anemiamea nui e pale aku i nā pilikia.
He aha ka maʻi maʻi anemia?
maʻi maʻi anemia He ʻāpana ia o ka 'hemoglobinopathy'. Hoʻomaka ka maʻi hemoglobinopathies ke loaʻa i ke kanaka hoʻokahi ʻano ʻokiʻoki "ʻino" beta-globin mai ka makua a me kekahi ʻano ʻano hemoglobin ʻē aʻe, e pili ana i ka hana ʻana o ke koko ʻulaʻula.
ʻO ka poʻe me ka maʻi sickle cell e hoʻopuka i ka hemoglobin abnormal. Hōʻike ʻia nā maʻi maʻi maʻi e ke ʻano o ka crescent-like, ʻano like ʻole ke ʻano o ke koko ʻulaʻula. ʻOi aku ka paʻakikī o kēia ʻano i ke kahe ʻana o ke koko ma nā ʻaʻa.
ʻOi aku ka paʻakikī a me ka maʻalahi o ke ʻano o ke koko ʻulaʻula. ʻOiai e hōʻemi ana kēia i ka hāʻawi ʻana i ka oxygen i loko o ke kino, ke kāohi nei ia i ke kahe koko.
ʻO wai ka maʻi maʻi maʻi anemia?
- Pilikia nā keiki i ka maʻi sickle cell inā loaʻa i nā mākua ʻelua ke ʻano sickle cell.
- ʻO ka poʻe e noho ana ma nā wahi me ka maʻi maʻi endemic, e like me ʻApelika, India, Mediterranean, a me Saudi Arabia, ʻoi aku ka nui o nā mea lawe.
He aha nā hōʻailona o ka sickle cell anemia?
Nā hōʻailona maʻi maʻi anemia Hōʻike pinepine ia e like me:
- Ka luhi a me ka nawaliwali
- ke ahi
- Ka pehu a me ka edema
- pōkole o ka hanu e paʻakikī ai ka neʻe ʻana, a ʻeha umauma
- ʻeha a me ka iwi
- Abdominal eha
- pilikia ʻike
- ʻO ka nausea, ka luaʻi a me ka ʻehaʻeha
- Ka hoʻokumu ʻana o nā ʻeha ma ka ʻili ma muli o ka maikaʻi ʻole o ke kahe koko
- hōʻailona jaundice
- hoʻonui ʻana i ka spleen
- ʻOi aku ka pōʻino o ke koko koko ma muli o kahi kīʻaha koko paʻa
- ʻOi aku ka nui o ka pōʻino o ka ate, ka pōʻino o ka puʻupaʻa, ka ʻeha a me nā pōhaku ʻōpū
- pili kino
- Nā pilikia o ka ulu ʻana o nā keiki, e like me ka pōkole o ke kumu e like me nā lima a me nā wāwae
- ʻOi aku ka nui o ka pilikia no ka hahau ʻana, ka hopu ʻana, a me nā hōʻailona e like me ka helu ʻana o nā lālā, ka paʻakikī o ka ʻōlelo ʻana, a me ka nalowale o ka ʻike.
- ʻOi aku ka pilikia no ka hoʻonui ʻana i ka puʻuwai a me ka ʻōhumu puʻuwai
ʻO nā kumu o ka maʻi maʻi anemia
maʻi maʻi anemia, He maʻi maʻi genetic. ʻAʻole ia ma muli o ka nohona a i ʻole nā kumu meaʻai, akā ma muli o ka hoʻoili ʻana i kekahi mau genes. o ke keiki maʻi maʻi anemiaNo ka loaʻa ʻana o ka maʻi, pono ia e hoʻoili i nā genes hemahema mai nā mākua ʻelua.
Ke hoʻoili ʻia ke keiki i kahi gene hemahema mai ka makua hoʻokahi wale nō, e loaʻa iā ia ka maʻi sickle cell akā ʻaʻole hōʻike i nā hōʻailona piha. He mea maʻamau kekahi mau koko ʻulaʻula a me ka hemoglobin. E deformed kekahi.
Pehea e mālama ʻia ai ka maʻi sickle cell anemia?
ʻOiai ʻaʻole hiki ke ho'ōla ʻia ka maʻi sickle cell, ʻo ka pahuhopu o ka lapaʻau "pilikia pilikiwi"ʻo ia ka hōʻemi i nā hōʻailona e pale a hoʻomaikaʻi i ka maikaʻi o ke ola.
pilikia pilikiwi a i ʻole inā loaʻa kahi pilikia, pono ka poʻe maʻi e noho i ka haukapila a nānā ʻia i ka wā e loaʻa ai nā wai a me nā lāʻau lapaʻau. ʻO ka hōʻailona maopopo loa ʻo ia ka hikiwawe, ke hou ʻana i ka ʻeha ma ka ʻōpū a me ka umauma. I kekahi mau hihia, pono paha ka mea maʻi i ka oxygen a me ke kahe koko. ʻO nā lāʻau lapaʻau ʻē aʻe:
- ʻO ka lāʻau hydroxyurea: Hoʻonui ia i ka hana ʻana o kahi ʻano hemoglobin, kahi e kōkua ai i ka pale ʻana i nā ʻulaʻula ʻulaʻula mai ka loaʻa ʻana o ke ʻano sickle.
- Ka hoʻololi ʻana o ka iwi iwi: Hiki ke kiʻi ʻia ka ʻiʻo iwi a i ʻole nā pūnaewele kumu mai kahi lālā o ka ʻohana i loaʻa ʻole ka maʻi a hoʻololi i ka maʻi. He hana pilikia kēia. Pono ia e lawe i nā lāʻau e hoʻopau ai i ka ʻōnaehana pale a pale i ke kino mai ka hakakā ʻana i nā cell transplanted.
- Gene therapy: Hana ʻia kēia ma ka hoʻokomo ʻana i nā genes i loko o nā pūnaewele precursor e hoʻohua mai i nā ʻāpana koko ʻulaʻula maʻamau.
Ka Lapaau Ma'amau o ka Anemia Sickle Cell
ʻai no ka anemia
ʻai, maʻi maʻi anemiaʻAʻole kōkua i ka hoʻomaikaʻi ʻana. Akā hiki iā ia ke mālama i nā hōʻailona a pale i nā pilikia hou aʻe. maʻi maʻi anemia Nā ʻōlelo aʻoaʻo meaʻai no:
- Loaʻa i nā calorie lawa.
- E ʻai i nā ʻano like ʻole a me nā huaʻai hou a me nā mea kanu.
- E ʻai i ka protein a me nā momona maikaʻi.
- E ʻai i nā meaʻai kiʻekiʻe i ka folate, kahi e kōkua ai i ka hana ʻana o nā ʻāpana koko ʻulaʻula.
- E ʻai i ka palaoa, legumes a me nā kumu protein holoholona e loaʻa ai ka nui o nā huaora B.
- Electrolyte imbalancesE inu i ka wai i kēlā me kēia lā e pale i ka wai a me ka wai.
- Mai ʻai i nā meaʻai i hana ʻia e like me nā meaʻai kō, nā kīʻaha i hoʻomaʻemaʻe ʻia, ka meaʻai wikiwiki, a me nā mea inu kō.
Ka hoʻohana ʻana i nā meaʻai meaʻai
Me ka meaʻai olakino a ʻano like ʻole, ʻōlelo ka poʻe loea i nā mea hoʻohui like ʻole e hiki ke mālama i nā hemahema, pale i nā iwi, a hāʻawi i nā hopena pale ʻē aʻe:
- Vitamin D
- kalipuna
- Folate/ʻakika folic
- ʻO ka Omega 3 fatty acids
- ʻO ka Vitamin B6 a me B12
- ʻO nā multivitamins me ke keleawe, ka zinc a me ka magnesium
ʻaila nui e hoʻemi i ka ʻeha
maʻi maʻi anemiahiki ke hana i ka ʻoʻoleʻa hui, nāwaliwali o ka ʻiʻo, ka ʻeha iwi, a me ka ʻeha o ka ʻōpū a i ʻole ka umauma. ʻAʻole ʻōlelo ʻia nā painkillers e hoʻohana pinepine ʻia no ka mea e hoʻopilikia maikaʻi lākou i ka hana ʻāʻī a me ka ate.
ʻaila nuiHoʻomaha ia i ka ʻeha a me ka mālama ʻana i ka ʻili i hoʻonāukiuki ʻia, hoʻomaikaʻi i ka pale ʻana a paipai i ka hoʻomaha.
ʻAila minetiHiki ke hoʻopili ʻia i ka ʻili e hōʻemi i ka ʻiʻo a me ka ʻeha hui. ʻO nā aila pono ʻē aʻe e kōkua ana i nā hōʻailona, ʻo ka frankincense e hōʻemi i ka mumū; Loaʻa iā ia nā aila citrus hōʻoluʻolu e like me ka lavender e hoʻomaha i ke kaumaha a me ka ʻalani a i ʻole ka hua waina e hōʻemi i ka luhi.
He aha nā pilikia o ka sickle cell anemia?
maʻi maʻi anemiaHoʻopilikia ia i nā pilikia koʻikoʻi i ka wā e hoʻopaʻa ai nā ʻili sickle i nā kīʻaha koko ma nā wahi like ʻole o ke kino. Hoʻopaʻa ʻeha a pōʻino paha nā pilikia pilikiwi Ua kapa.
Eia keia maʻi maʻi anemiaNā kūlana e hiki mai ana mai:
- anemia nui
- maʻi lima-wāwae
- hoʻopaʻa ʻana i ka spleen
- Hoʻopaneʻe ka ulu ʻana
- ʻO nā pilikia neurological e like me ka hopu a me ka hahau
- pilikia maka
- ʻeha ʻili
- ʻO ka maʻi puʻuwai a me ka maʻi maʻi umauma
- maʻi māmā
- Priapism
- pōhaku ʻōpū
- sickle chest syndrome
ʻO nā kānaka me ka maʻi maʻi maʻi anemiaʻoi aʻe ka pilikia o ka hoʻomohala ʻana i nā maʻi a me nā maʻi. He mea nui e noho kaawale keia poe mai ka poe mai. ʻO ka holoi pinepine ʻana i kou mau lima, kaʻawale i ka wela a me ke anuanu, ʻaʻole hoʻoikaika kino, loaʻa ka hiamoe a me ka inu ʻana i ka wai nā mea e noʻonoʻo ai.
Inā loaʻa kekahi o kēia mau hōʻailona (ʻoi loa i nā keiki), e ʻimi koke i ka ʻōlelo aʻoaʻo olakino:
- ke kuni ma luna o 38.5 °C
- Paʻakikī ka hanu a me ka ʻeha ma ka umauma a me ka ʻōpū
- ʻO ke poʻo koʻikoʻi, loli ka ʻike, a paʻakikī i ka noʻonoʻo ʻana
- Nānā