Iyini I-Sickle Cell Anemia, Ibangelwa Yini? Izimpawu Nokwelashwa

I-sickle cell anemiawuhlobo lwesifo esitholakala ngofuzo se-sickle cell. Kuthinta amangqamuzana egazi abomvu kanye nephrotheni ebizwa ngokuthi i-hemoglobin. Ngoba kungokwefa, okunye i-anemia izinhlobo ezahlukene. Ngoba iwufuzo futhi isuka kubazali iye ezinganeni zabo.

Khona manje ukwelashwa kwe-sickle cell anemia akukho. Kunezinketho zokwelapha zokuphatha izimpawu nokunciphisa izinkinga.

iziguli ezine-sickle cell anemiaIngxenye ebalulekile yensimbi, i-zinc, Ithusii-folic acid, i-pyridoxine, i-vitamin D kanye Vitamin E njengokushoda kwezakhamzimba. 

Ukudla okulinganiselayo; njengokulibaziseka ukukhula nokuthuthuka, ukuncipha kwamathambo, ukwanda kwengozi yokuphuka, izinkinga zombono, ukungenwa yizifo. I-sickle cell anemiakubalulekile ukuvimbela izinkinga.

Iyini i-sickle cell anemia?

I-sickle cell anemia Kuyingxenye ye-'hemoglobinopathy '. I-Hemoglobinopathies iqala lapho umuntu ezuza njengefa okungenani isakhi sofuzo se-beta-globin "esinesici" esisodwa kumzali kanye nolunye ufuzo lwe-hemoglobin olungajwayelekile, oluthinta indlela amangqamuzana abomvu egazi asebenza ngayo.

Labo abanesifo se-sickle cell bakhiqiza i-hemoglobin engavamile. Izifo zama-sickle cell zibonakala ngamaseli abomvu egazi akhubazekile amise okwe-crescent, anomumo ngendlela engavamile. Lesi simo senza kube nzima ukuthi igazi lidlule emithanjeni.

Amangqamuzana egazi abomvu amise okwesikela aqinile futhi ayaphuka. Nakuba lokhu kunciphisa ukutholakala komoyampilo emzimbeni, kuvimbela ukugeleza kwegazi.

Ubani othola i-sickle cell anemia?

• Izingane zisengozini yokuthola isifo se-sickle cell uma bobabili abazali benesici se-sickle cell.
• Abantu abahlala ezindaweni ezinomalaleveva oyinsakavukela, njenge-Afrika, i-India, i-Mediterranean, ne-Saudi Arabia, banamathuba amaningi okuba ngabathwali.

Yiziphi izimpawu ze-sickle cell anemia?

Izimpawu ze-Sickle cell anemia Ngokuvamile kubonakala kanje:

• Ukukhathala nobuthakathaka
• umlilo
• Ukuvuvukala kanye ne-edema
• ukuphelelwa umoya okwenza kube nzima ukunyakaza, futhi ubuhlungu besifuba
• ubuhlungu bamalunga namathambo
• Ubuhlungu besisu
• izinkinga zokubona
• Isicanucanu, ukuhlanza kanye nokuphazamiseka kokugaya ukudla 
• Ukwakhiwa kwamanxeba esikhumbeni ngenxa yokungahambi kahle kwegazi
• izimpawu ze-jaundice
• ukwanda ubende
• Ingozi ephezulu yamahlule egazi ngenxa yemithambo yegazi evalekile
• Ingozi ephezulu yokulimala kwesibindi, ukulimala kwezinso, ukulimala kwamaphaphu kanye namatshe enyongo
• ukungasebenzi kahle kwezocansi
• Izinkinga zokukhula ezinganeni, njengokufinyezwa kwe-trunk ngokulingana nezingalo nemilenze
• Ingozi ephezulu yokushaywa unhlangothi, ukuquleka, kanye nezimpawu ezifana nokuba ndikindiki ezithweni, ubunzima bokukhuluma, nokulahlekelwa ukwazi.
• Ingozi ephezulu yokwanda kwenhliziyo nokububula kwenhliziyo

Izinkinga ze-sickle cell anemia

i-sickle cell anemia, Kuyinkinga yofuzo. Akubangelwa indlela yokuphila noma izici zokudla okunomsoco, kodwa ukuzuza ufuzo oluthile. wengane I-sickle cell anemiaUkuze ithole lesi sifo, kumelwe izuze izakhi zofuzo ezinesici kubo bobabili abazali.

Lapho ingane izuza isakhi sofuzo esinesici kumzali oyedwa kuphela, izoba nesifo se-sickle cell kodwa ingabonisi izimpawu ezigcwele. Amanye amangqamuzana egazi abomvu kanye ne-hemoglobin kuzoba yinto evamile. Abanye bazokhubazeka.

Yelashwa kanjani i-sickle cell anemia?

Njengoba isifo se-sickle cell singelapheki, umgomo wokwelashwa uthi "i-sickle cell crisis” uwukunciphisa izimpawu zokuvimbela nokwenza ngcono izinga lempilo. 

i-sickle cell crisis noma uma kuvela isimo esiphuthumayo, iziguli kudingeka zihlale esibhedlela futhi ziqashwe lapho zithola uketshezi nemithi. Uphawu olusobala kakhulu ukuzuma, ukugwaza izinhlungu ezibukhali esiswini nasesifubeni. Kwezinye izimo, isiguli singase sidinge umoya-mpilo kanye nokumpontshelwa igazi. Ezinye izindlela zokwelapha zihlanganisa:

• Isidakamizwa se-Hydroxyurea: Yandisa ukukhiqizwa kohlobo lwe-hemoglobin, esiza ukuvimbela amangqamuzana egazi abomvu ekubeni amise okwesikela.

• Ukufakelwa komnkantsha wamathambo: Umnkantsha noma ama-stem cells angatholwa ilungu lomndeni elingenaso lesi sifo bese lifakelwa esigulini. Lena inqubo eyingozi. Kudinga ukuphuza imithi ecindezela amasosha omzimba futhi ivimbele umzimba ekulweni namaseli atshalwe kabusha.

• Ukwelashwa kofuzo: Lokhu kwenziwa ngokufaka izakhi zofuzo kumangqamuzana angaphambili akhiqiza amangqamuzana egazi abomvu avamile.

Ukwelashwa Kwemvelo Kwe-Sickle Cell Anemia

Ukudla kwe-anemia

Ukudla okunomsoco, I-sickle cell anemiaAkusizi ukuthuthukisa. Kodwa ivumela ukuphatha izimpawu nokuvimbela ezinye izinkinga. I-sickle cell anemia Amathiphu wokudla okunempilo:

• Thola amakhalori anele. 
• Yidla izithelo nemifino eminingi ehlukahlukene.
• Yidla amaprotheni anele namafutha anempilo. 
• Yidla ukudla okune-folate eningi, esiza ukukhiqizwa kwamangqamuzana egazi abomvu.
• Yidla okusanhlamvu, okusanhlamvu okusanhlamvu kanye nemithombo yamaprotheni ezilwane ukuze uthole amavithamini B anele.
• Ukungalingani kwe-ElectrolytePhuza amanzi anele usuku ngalunye ukuvimbela ukuphelelwa amanzi emzimbeni kanye nokuphelelwa amanzi emzimbeni.  
• Ungakudli ukudla okugayiwe njengoshukela, okusanhlamvu okucolisisiwe, ukudla okusheshayo, neziphuzo ezinoshukela.

Ukusetshenziswa kwesengezo sokudla okunomsoco

Kanye nokudla okunempilo nokuhlukahlukene, ochwepheshe batusa izinhlobonhlobo zezithako ezingakwazi ukwelapha ukuntula, ukuvikela amathambo, nokuhlinzeka ngeminye imiphumela yokuzivikela:

• Ivithamini D
• calcium
• I-folate/folic acid
• I-Omega 3 fatty acids
• Amavithamini B6 no-B12
• Ama-multivitamins anethusi, i-zinc ne-magnesium

amafutha abalulekile ukunciphisa ubuhlungu

I-sickle cell anemiakungabangela ukuqina kwamalunga, ubuthakathaka bemisipha, ubuhlungu bamathambo, nobuhlungu besisu noma besifuba. Ama-painkillers awanconywa ukuthi asetshenziswe njalo ngoba azophazamisa ukusebenza kwezinso nesibindi. 

amafutha abalulekileIqeda ubuhlungu kanye nokuphatha isikhumba esithukuthele, ithuthukisa amasosha omzimba futhi ikhuthaze ukuphumula.

Amafutha e-MintIngasetshenziswa esikhumbeni ukunciphisa ubuhlungu bemisipha namalunga. Amanye amafutha abalulekile asiza ngezimpawu ahlanganisa inhlaka yempepho ukunciphisa ukuvuvukala; Inamafutha e-citrus aqabulayo afana ne-lavender ukukhulula ingcindezi kanye ne-orange noma i-grapefruit ukunciphisa ukukhathala.

Yiziphi izinkinga ze-sickle cell anemia?

I-sickle cell anemiaKudala izinkinga ezinkulu ezenzeka lapho ama-sickle cell evala imithambo yegazi ezingxenyeni ezihlukene zomzimba. Ukuvinjwa okubuhlungu noma okulimazayo izinkinga ze-sickle cell It ngokuthi.

Okulandelayo kukhona I-sickle cell anemiaIzimo ezingase zivele:

• i-anemia enzima
• i-hand-foot syndrome
• ukususwa kwe-spleen
• Ukukhula okubambezelekile
• Izinkinga ze-neurological ezifana nokuquleka nokushaywa unhlangothi
• izinkinga zamehlo
• izilonda zesikhumba
• Isifo senhliziyo kanye nesifo sesifuba
• isifo samaphaphu
• I-Priapism
• inyongo
• i-sickle chest syndrome

Abantu abane-sickle cell anemiafuthi babe sengozini enkulu yokuthola izifo kanye nezifo. Kubalulekile ukuthi laba bantu baqhelelane nabantu abagulayo. Ukugeza izandla njalo, ukugwema ukushisa nokubanda okukhulu, ukungazivocavoci kakhulu, ukulala ngokwanele nokuphuza amanzi anele yikona okuzocatshangelwa.

Uma kuvela noma yiziphi izimpawu ezilandelayo (ikakhulukazi ezinganeni), funa iseluleko sezokwelapha ngokushesha:

• ukushisa okungaphezu kuka-38.5 ° C
• Ukuphefumula kanzima nobuhlungu esifubeni nasesiswini
• Ikhanda elibuhlungu elibuhlungu, ukushintsha kombono, nobunzima bokugxila
• Bhekisisani