Menene Sickle Cell Anemia, Me Ke Hana Ta? Alamomi da Magani

sickle cell anemianau'in cutar sikila ce da aka gada. Yana shafar jajayen ƙwayoyin jini da furotin da ake kira haemoglobin. Domin gado ne, sauran karancin jini iri daban-daban. Domin shi kwayoyin halitta ne kuma yana wucewa daga iyaye zuwa ga 'ya'yansu.

A yanzu haka maganin sikila anemia babu. Akwai zaɓuɓɓukan magani don sarrafa alamun cutar da rage rikitarwa.

yana haifar da anemia na sikila

marasa lafiya na sickle cell anemiaWani muhimmin sashi na baƙin ƙarfe, zinc, Copper, folic acid, pyridoxine, bitamin D da kuma Vitamin E kamar rashin abinci mai gina jiki. 

Daidaitaccen abinci; irin su jinkirin girma da ci gaba, rage yawan kashi, ƙara yawan haɗarin karaya, matsalolin hangen nesa, mai sauƙi ga cututtuka. sickle cell anemiamahimmanci don hana rikitarwa.

Menene sikila anemia?

sickle cell anemia Yana daga cikin 'hemoglobinopathy'. Haemoglobinopathies suna tasowa ne lokacin da mutum ya gaji aƙalla kwayar cutar sikila (S) beta-globin guda ɗaya daga iyaye da kuma wani ƙwayar haemoglobin mara kyau, wanda ke shafar yadda ƙwayoyin jajayen jini ke aiki.

Wadanda ke da cutar sikila suna haifar da haemoglobin mara kyau. Cututtukan sikila suna da nakasu mai sifar jinjirin wata, sifar jajayen jinin da ba su saba ba. Wannan siffar yana sa jini ya yi wuya ya wuce ta jijiyoyi.

Kwayoyin jajayen jini masu sikila sun fi wuya kuma sun gagara. Duk da yake wannan yana rage iskar oxygen a cikin jiki, yana hana kwararar jini.

Wanene ke samun sikila anemia?

  • Yara suna fuskantar haɗarin kamuwa da cutar sikila idan duka iyaye biyu suna da halin sikila.
  • Mutanen da ke zaune a yankuna masu fama da zazzabin cizon sauro, irin su Afirka, Indiya, Bahar Rum, da Saudi Arabiya, sun fi zama masu ɗauke da cutar.

menene alamun cutar sikila anemia

Menene alamun anemia na sikila?

Alamun sikila anemia Yawanci yana bayyana kamar:

  • Gajiya da rauni
  • wuta
  • Kumburi da edema
  • karancin numfashi wanda ke sa da wuyar motsawa, kuma ciwon kirji
  • hadin gwiwa da ciwon kashi
  • Ciwon ciki
  • matsalolin hangen nesa
  • Tashin zuciya, amai da bacin rai 
  • Samuwar raunuka a kan fata saboda rashin kyaututtukan jini
  • jaundice bayyanar cututtuka
  • kara girman kwaya
  • Haɗari mafi girma ga gudan jini saboda toshewar jijiyar jini
  • Haɗari mafi girma ga lalacewar hanta, lalacewar koda, lalacewar huhu da gallstones
  • rashin aikin jima'i
  • Matsalolin ci gaba a cikin yara, kamar gajarta ganga daidai da hannaye da ƙafafu
  • Haɗari mafi girma ga bugun jini, kamewa, da alamu kamar sumsuwa a cikin gaɓoɓi, wahalar magana, da asarar sani.
  • Haɗari mafi girma don ƙara girman zuciya da gunaguni na zuciya

Abubuwan da ke haifar da anemia na sikila

sickle cell anemia, cuta ce ta kwayoyin halitta. Ba ta hanyar salon rayuwa ko abubuwan gina jiki ke haifar da ita ba, amma ta hanyar gadon wasu kwayoyin halitta. na yaro sickle cell anemiaDon kamuwa da cutar, dole ne ta gaji marasa lahani daga iyaye biyu.

Lokacin da yaro ya gaji rashin lahani daga iyaye ɗaya kawai, za su kamu da cutar sikila amma ba za su nuna cikakkiyar alamun ba. Wasu jajayen ƙwayoyin jini da haemoglobin za su kasance al'ada. Wasu kuma za su lalace.

fasali na sickle cell anemia

Yaya ake bi da sikila anemia?

Tunda cutar sikila ba za a iya warkewa ba, manufar magani ita ce "rikicin sikila” shine don rage alamun cutar don hanawa da inganta rayuwa. 

rikicin sikila ko kuma idan gaggawa ta faru, marasa lafiya suna buƙatar zama a asibiti kuma a kula da su yayin karbar ruwa da magunguna. Alamar da ta fi fitowa fili ita ce kwatsam, tana soka raɗaɗi masu kaifi a ciki da ƙirji. A wasu lokuta, majiyyaci na iya buƙatar iskar oxygen da kuma ƙarin jini. Sauran jiyya sun haɗa da:

  • Magungunan Hydroxyurea: Yana ƙara samar da wani nau'i na haemoglobin, wanda ke taimakawa hana jajayen ƙwayoyin jini daga samun sifar sikila.
  • Dashen kasusuwa: Za a iya samun maƙarƙashiyar ƙashi ko ƙananan ƙwayoyin cuta daga dangin da ba shi da cutar kuma a dasa shi cikin majiyyaci. Wannan hanya ce mai haɗari. Yana buƙatar shan magungunan da ke hana tsarin rigakafi da kuma hana jiki daga yaki da kwayoyin da aka dasa.
  • Maganin Halitta: Ana yin haka ta hanyar dasa kwayoyin halitta a cikin sel na farko waɗanda ke samar da ƙwayoyin jajayen jinin al'ada.

Maganin Halitta na Sickle Cell Anemia

abubuwan haɗarin sickle cell anemia

rage cin abinci don anemia

Abinci mai gina jiki, sickle cell anemiaBa ya taimaka inganta. Amma yana ba da damar sarrafa alamun bayyanar cututtuka da kuma hana ƙarin rikitarwa. sickle cell anemia Nasihun abinci don:

  • Samun isassun adadin kuzari. 
  • Ku ci iri-iri da yalwar sabbin 'ya'yan itatuwa da kayan marmari.
  • Ka sha isassun furotin da mai mai lafiya. 
  • Cin abinci mai yawan folate, wanda ke taimakawa samar da jajayen ƙwayoyin jini.
  • Yi amfani da hatsi, legumes da tushen furotin na dabba don samun isasshen bitamin B.
  • Rashin daidaituwa na ElectrolyteA sha isasshen ruwa kowace rana don hana bushewa da bushewa.  
  • Kada ku ci abinci da aka sarrafa kamar abinci mai sikari, tsayayyen hatsi, abinci mai sauri, da abubuwan sha masu zaki.

Amfani da kari na abinci

Tare da lafiyayyen abinci iri-iri, masana suna ba da shawarar nau'ikan kari waɗanda zasu iya magance rashi, kare ƙasusuwa, da samar da wasu abubuwan kariya:

  • Vitamin D
  • alli
  • Folate/folic acid
  • Omega 3 fatty acid
  • Vitamin B6 da B12
  • Multivitamins tare da jan karfe, zinc da magnesium

muhimmanci mai don rage zafi

sickle cell anemiana iya haifar da taurin haɗin gwiwa, raunin tsoka, ciwon kashi, da ciwon ciki ko ƙirji. Ba a ba da shawarar yin amfani da magungunan kashe zafi akai-akai saboda za su yi illa ga ayyukan koda da hanta. 

muhimmanci maiYana sauƙaƙa ciwo tare da magance fushin fata, inganta rigakafi da haɓaka shakatawa.

Mint manAna iya shafa shi ga fata don rage tsoka da ciwon haɗin gwiwa. Sauran mahimman mai da ke taimakawa tare da bayyanar cututtuka sun haɗa da turaren wuta don rage kumburi; Yana da man citrus masu wartsake kamar lavender don sauƙaƙa damuwa da orange ko innabi don rage gajiya.

Wanene ke samun sikila anemia?

Menene matsalolin sikila anemia?

sickle cell anemiaYana haifar da rikice-rikice masu tsanani waɗanda ke faruwa lokacin da ƙwayoyin sikila suka toshe hanyoyin jini a sassa daban-daban na jiki. Katange mai raɗaɗi ko ɓarna rikicin sikila Yana kira.

Wadannan su ne sickle cell anemiaSharuɗɗan da za su iya tasowa daga:

  • anemia mai tsanani
  • ciwon ƙafar hannu
  • saiwa sequestration
  • Jinkiri girma
  • Rikice-rikicen jijiyoyi kamar su bugun jini da bugun jini
  • matsalolin ido
  • ciwon fata
  • Ciwon zuciya da ciwon kirji
  • cutar huhu
  • Priapism
  • gallstones
  • sickle kirji ciwo

sickle cell anemia magani na halitta

Mutanen da ke da ciwon sikilaHakanan suna da haɗarin haɓaka cututtuka da cututtuka. Yana da mahimmanci waɗannan mutane su nisanci marasa lafiya. Wanke hannu akai-akai, nisantar matsanancin zafi da sanyi, rashin motsa jiki mai tsanani, samun isasshen barci da shan isasshen ruwa sune abubuwan da yakamata a yi la'akari dasu.

Idan daya daga cikin wadannan alamomin ya bayyana (musamman a cikin yara), nemi shawarar likita nan da nan:

  • zazzabi sama da 38.5 ° C
  • Wahalar numfashi da zafi a ƙirji da ciki
  • Ciwon kai mai tsanani, canjin gani, da wahalar maida hankali
  • Kalli
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