He aha ka maʻi o Wilson, ke kumu? Nā hōʻailona a me ka lapaʻau

ʻO ka maʻi o Wilson, kou kino me ka hao He maʻi hoʻoilina kakaʻikahi e hoʻopau i ke koena o ke keleawe a me ke keleawe. Loaʻa ka maʻi i nā kānaka ma waena o 5 a 35 mau makahiki. Ua loaʻa pū i nā poʻe ʻōpio a me nā poʻe ʻelemakule. He maʻi hiki ke mālama ʻia ke ʻike mua ʻia.

He aha ka ma'i o Wilson?

ʻO kēia maʻi ke kumu o ka hōʻiliʻili ʻana o ka nui o ke keleawe i loko o ke kino, ʻoi aku hoʻi i loko o ke ake, lolo, a me nā maka. Hana pinepine ia ma waena o nā makahiki 5 a me 35. ʻO ke kūlana ke kumu o nā pilikia neurological a me ka psychiatric a me ka maʻi ate. 

keleawe; He mea nui ia no ka ulu ʻana o nā aʻalolo, iwi, collagen a me melanin pigment i ka ʻili. Hoʻopili ʻia ke keleawe mai ka meaʻai a hoʻokuʻu ʻia ke koena mai ke kino ma o ka bile i hana ʻia i loko o ke ake.

ʻO ka maʻi o Wilsonpale i ka hoopau pono ia ke keleawe. ʻO ka hopena, loaʻa ka ʻili keleawe; He kūlana weliweli kēia.

He aha ke kumu o ka maʻi o Wilson?

ʻO ka hoʻololi ʻana i ka gene ATP7B ke kumu o kēia maʻi. He maʻi genetic ia, i hoʻoholo ʻia e ʻelua genes, hoʻokahi mai ka makuahine a ʻo kekahi mai ka makua kāne.

Hana ʻia ʻo ATPase 2 e lawe ana i ke keleawe mai kēia gene a komo i ka lawe ʻana i ke keleawe mai ke ake a i nā wahi ʻē aʻe o ke kino.

ʻO ka maʻi o Wilsonua hoʻoili ʻia ma ke ʻano he autosomal recessive trait. ʻO ia hoʻi, no ka ulu ʻana o ka maʻi, pono nā mākua ʻelua e lawe i ka gene defect. ʻAʻole loaʻa ka maʻi i ka poʻe i hoʻoili i hoʻokahi gene abnormal, lilo lākou i mea lawe a hāʻawi i ka gene i kā lākou mau keiki.

He aha nā hōʻailona o ka maʻi o Wilson?

Aia kēia maʻi i ke kanaka mai ka hānau ʻana. Akā ʻaʻole ia e hōʻike i nā hōʻailona a hiki i ka ulu ʻana o ke keleawe i loko o ka lolo, ate, a i ʻole nā ​​mea ʻē aʻe.

ʻOkoʻa nā hōʻailona o ka maʻi e like me ka ʻāpana o ke kino i hoʻopilikia ʻia. Nā hōʻailona o ka maʻi o Wilson penei:

Nā hōʻailona o ka ate:

• Nawaliwali
• lilo kaumaha
• nausea, luai
• ʻAnorexia
• Kāwili
• melemele o ka ʻili
• ʻO Edema
• Abdominal eha
• pehu
• Ka hoʻokumu ʻana o nā kīʻaha koko e like me ka punawelewele i loko o ka ʻili
• ʻūhā ʻiʻo

 Ke kūkulu ʻia ke keleawe i loko o ka lolo, ʻike ʻia kēia mau hōʻailona neurological: 

• Ka hoʻomanaʻo, ka ʻōlelo a i ʻole ka ʻike maka
• Hoʻololi o ka hele ʻana
• ʻO Migraine
• Kuha
• ʻO ka hiamoe
• paʻakikī i ka hoʻohana ʻana i nā lima
• hoʻololi kanaka
• loli ka manaʻo
• Kaumaha
• ʻO ka hopu ʻana a me ka ʻeha ʻiʻo i nā pae kiʻekiʻe

Nā hōʻailona maka: 

• Nā apo ʻo Kayser-Fleischer
• cataract

Nā hōʻailona i loaʻa ma muli o ka hōʻiliʻili keleawe i loko o nā kino ʻē aʻe:

• Ka ʻulaʻula o nā kui
• Pohaku hakuʻala
• osteoporosis mua
• Pākuʻi
• nā hana ʻino ʻole o ka haʻi ʻana
• ke koko haʻahaʻa

He aha nā pilikia o ka maʻi o Wilson?

He mea make kēia maʻi ke mālama ʻole ʻia. Hoʻopilikia ia i nā hopena koʻikoʻi e like me:

• ʻO ka hemahema o ke ake e hiki koke mai a ulu mālie paha i nā makahiki
• cirrhosis o ke ake
• ʻO ka haʻalulu, ka neʻe ʻana o ka ʻiʻo i makemake ʻole ʻia, ka hele ʻana a me nā pilikia ʻōlelo
• pilikia kīkī
• ʻO nā loli o ke kanaka, ke kaumaha, ka huhū, bipolar kāna hananā pilikia pili kino e like me psychosis
• ʻO nā pilikia koko e hoʻoulu ai i ka anemia a me ka jaundice, e like me ka hemolysis

Pehea e ʻike ʻia ai ka maʻi o Wilson?

ʻO ka maʻi o Wilsonpaʻakikī ke ʻike. No ka mea, huikau kona mau hōʻailona me nā maʻi ʻē aʻe e like me ka hepatitis. 

Hana ʻia ka ʻike ma muli o ka hui pū ʻana o nā hōʻailona a me nā hopena hōʻike. ʻO nā hoʻāʻo i hoʻohana ʻia e ʻike i kēia maʻi:

• koko a me ka mimi
• Hōʻike maka
• Wehe i kahi laʻana o ka ʻiʻo o ke ake no ka hoʻāʻo ʻana (biopsy)
• hoʻāʻo genetic

ʻO ka maʻi maʻi o Wilson

• Paipai ke kauka i nā lāʻau i kapa ʻia he chelating agents e hoʻopaʻa i ke keleawe a hoʻokuʻu i loko o ke kahe koko. Ma kēia ala, kānana nā puʻupaʻa i ke keleawe a hoʻokuʻu i loko o ka mimi. 
• Hoʻopili ka mālama ʻana i ka pale ʻana i ke keleawe mai ka hōʻiliʻili hou ʻana. 
• I nā hihia koʻikoʻi, pono ke hoʻololi i ke akepaʻa.
• ʻO ka maʻi o WilsonHoʻohana ʻia nā lāʻau no ke ola. Hiki i ke kauka ke kuhikuhi i nā lāʻau ʻē aʻe no ka hoʻopau ʻana i ka hōʻailona.

ʻO ka maʻi o Wilson i ka home

ʻAʻohe mālama home no kēia maʻi. Makemake ke kauka e kaupalena i ka lawe ʻana i ke keleawe mai ka meaʻai. Inā loaʻa iā ʻoe nā paipu keleawe ma kou home, he manaʻo maikaʻi e hoʻāʻo ʻia kāu wai paipu no nā pae keleawe. ʻAʻole pono e hoʻohana ʻia nā multivitamins me ke keleawe.

ʻO nā meaʻai i loaʻa ka nui o ke keleawe:

• Akepaʻa
• iʻa iʻa
• Fish
• Nati
• kokoleka
• Hua maloʻo

Nā kūmole: 1