Sickle Cell Anemia ke Eng, E Baka Eng? Matšoao le Phekolo

sickle cell anemiake mofuta oa lefu le futsitsoeng la sickle cell. E ama lisele tse khubelu tsa mali le protheine e bitsoang hemoglobin. Hobane ke lefutso, tse ling khaello ea mali mefuta e fapaneng. Hobane ke liphatsa tsa lefutso 'me li fetisoa ho tloha ho batsoali ho ea ho bana ba bona.

Hona joale kalafo ya sickle cell anemia ha ho letho. Ho na le mekhoa ea phekolo ea ho laola matšoao le ho fokotsa mathata.

e bakang sickle cell anemia

batho ba nang le lefu la anemiaKarolo e kholo ea tšepe, zinki, Koporo, folic acid, pyridoxine, vithamine D le Vithamine E joalo ka khaello ea limatlafatsi. 

Lijo tse leka-lekaneng; tse kang ho lieha ho hōla le tsoelo-pele, ho fokotseha ha masapo, kotsi e eketsehileng ea ho robeha, mathata a pono, ho ba le tšoaetso ea mafu. sickle cell anemiabohlokoa ho thibela mathata.

Sickle cell anemia ke eng?

sickle cell anemia Ke karolo ea 'hemoglobinopathy'. Hemoglobinopathies e ba teng ha motho a futsa bonyane phatsa e le 'ngoe ea "sekele e senyehileng" (S) ea beta-globin ho motsoali le e 'ngoe e sa tloaelehang ea hemoglobin, e amang tsela eo lisele tse khubelu tsa mali li sebetsang ka eona.

Ba nang le lefu la sickle cell ba hlahisa hemoglobin e sa tloaelehang. Mafu a sickle cell a tšoauoa ka lisele tse khubelu tsa mali tse holofetseng tse nang le sebōpeho sa crescent, tse nang le sebōpeho se sa tloaelehang. Sebopeho sena se etsa hore ho be thata hore mali a fete ka har'a methapo.

Lisele tse khubelu tsa mali tse nang le sebōpeho sa sekele li thatafala ebile lia robeha. Le hoja sena se fokotsa phepelo ea oksijene ’meleng, se sitisa phallo ea mali.

Ke mang ea fumanang sickle cell anemia?

  • Bana ba kotsing ea ho tšoaroa ke lefu la sickle cell haeba batsoali ka bobeli ba na le tšobotsi ea sickle cell.
  • Batho ba lulang libakeng tse nang le lefu la malaria, tse kang Afrika, India, Mediterranean le Saudi Arabia, ho na le monyetla o moholo oa hore e be bajari.

matšoao a sickle cell anemia ke afe

Matšoao a sickle cell anemia ke afe?

Matšoao a sickle cell anemia Hangata e bonahala e le:

  • Mokhathala le bofokoli
  • mollo
  • Ho ruruha le edema
  • ho hema ka thata e etsang hore ho be thata ho sisinyeha, le bohloko ba sefuba
  • bohloko ba manonyeletso le masapo
  • Bohloko ba mpeng
  • mathata a pono
  • Ho nyekeloa ke pelo, ho hlatsa le tšilo ea lijo 
  • Ho thehoa ha maqeba letlalong ka lebaka la phallo e mpe ea mali
  • matšoao a jaundice
  • ho hola ha spleen
  • Kotsi e kholo ea ho koala mali ka lebaka la mothapo o koetsoeng oa mali
  • Kotsi e kholo ea ho senyeha ha sebete, ho senyeha ha liphio, ho senyeha ha matšoafo le nyooko
  • ho se sebetse hantle ka thobalano
  • Mathata a nts'etsopele ho bana, joalo ka ho khutsufatsa kutu ho ea ka matsoho le maoto
  • Kotsi e kholo ea ho tšoaroa ke stroke, ho tsietsana, le matšoao a joalo ka bohatsu maotong le matsoho, bothata ba ho bua le ho lahleheloa ke kelello.
  • Kotsi e kholo ea ho korotla ha pelo le pelo e atolositsoeng

Lisosa tsa sickle cell anemia

sickle cell anemia, Ke bothata ba liphatsa tsa lefutso. Ha e bakoe ke mokhoa oa bophelo kapa mekhoa ea phepo e nepahetseng, empa ke ho rua liphatsa tsa lefutso tse itseng. tsa ngoana sickle cell anemiaHo fumana lefu lena, le tlameha ho futsa liphatsa tsa lefutso tse nang le bokooa ho batsoali ka bobeli.

Ha ngoana a futsa lefutso le nang le bokooa ho motsoali a le mong feela, o tla ba le lefu la sickle cell empa a sa bontše matšoao a feletseng. Lisele tse ling tse khubelu tsa mali le hemoglobin li tla ba tse tloaelehileng. Ba bang ba tla holofala.

likarolo tsa sickle cell anemia

Sickle cell anemia e phekoloa joang?

Kaha lefu la sickle cell ha le phekolehe, sepheo sa kalafo ke "maqakabetsi a lisele tse hlabang” ke ho fokotsa matšoao ho thibela le ho ntlafatsa boleng ba bophelo. 

maqakabetsi a lisele tse hlabang kapa haeba ho hlaha boemo ba tšohanyetso, bakuli ba lokela ho lula sepetlele le ho behoa leihlo ha ba ntse ba fuoa maro le meriana. Letšoao le totobetseng ka ho fetisisa ke la tšohanyetso, ho hlaba mahlaba a bohale ka mpeng le sefuba. Maemong a mang, mokuli a ka ’na a hloka oksijene hammoho le tšelo ea mali. Liphekolo tse ling li kenyelletsa:

  • Setlhare sa Hydroxyurea: E eketsa tlhahiso ea mofuta oa hemoglobin, e thusang ho thibela lisele tse khubelu tsa mali ho ba le sebopeho sa sekele.
  • Ho fetisoa ha moko oa masapo: Lisele tsa 'mele kapa tsa stem li ka fumanoa ho setho sa lelapa se se nang lefu lena ebe se fetisetsa ho mokuli. Ena ke mokhoa o kotsi. E hloka ho noa meriana e hatellang sesole sa 'mele le ho thibela 'mele ho loantša lisele tse fetisitsoeng.
  • Phekolo ea liphatsa tsa lefutso: Sena se etsoa ka ho kenya liphatsa tsa lefutso liseleng tsa pele tse hlahisang lisele tse khubelu tsa mali tse tloaelehileng.

Kalafo ea Tlhaho ea Sickle Cell Anemia

Mabaka a kotsi a sickle cell anemia

lijo bakeng sa phokolo ea mali

Phepo, sickle cell anemiaHa e thuse ho ntlafatsa. Empa e lumella ho laola matšoao le ho thibela mathata a mang. sickle cell anemia Litlhahiso tsa phepo e nepahetseng bakeng sa:

  • Fumana lik'halori tse lekaneng. 
  • E-ja mefuta e mengata ea litholoana le meroho e mecha.
  • Ja liprotheine tse lekaneng le mafura a phetseng hantle. 
  • Ja lijo tse nang le folate e ngata, e thusang tlhahiso ea lisele tse khubelu tsa mali.
  • Sebelisa lijo-thollo, linaoa le mehloli ea liprotheine tsa liphoofolo ho fumana livithamine tsa B tse lekaneng.
  • Ho se leka-lekane ha electrolyteNoa metsi a lekaneng letsatsi ka leng ho thibela ho felloa ke metsi 'meleng le ho tsoa 'meleng.  
  • U se ke ua ja lijo tse feliloeng tse kang lijo tse tsoekere, lijo-thollo tse hloekisitsoeng, lijo tse potlakileng le lino tse tsoekere.

Tšebeliso ea phepo e nepahetseng

Hammoho le lijo tse phetseng hantle le tse fapaneng, litsebi li khothaletsa mefuta e fapaneng ea li-supplement tse ka phekolang bofokoli, ho sireletsa masapo le ho fana ka litlamorao tse ling tsa tšireletso:

  • Vithamine D
  • k'halsiamo
  • Folate/folic acid
  • Omega 3 fatty acids
  • Vithamine B6 le B12
  • Li-multivitamine tse nang le koporo, zinki le magnesium

oli ea bohlokoa ho fokotsa bohloko

sickle cell anemiae ka baka ho satalla ha manonyeletso, ho fokola ha mesifa, ho opeloa ke masapo, le mahlaba ka mpeng kapa sefubeng. Li-painkillers ha li khothalletsoe hore li sebelisoe khafetsa kaha li tla ama ts'ebetso ea liphio le sebete hampe. 

oli ea bohlokoaE kokobetsa bohloko hammoho le ho tšoara letlalo le hlabang, e ntlafatsa ho itšireletsa mafung le ho khothalletsa phomolo.

Oli ea koenaE ka sebelisoa letlalong ho fokotsa bohloko ba mesifa le manonyeletso. Lioli tse ling tsa bohlokoa tse thusang ka matšoao li kenyelletsa libano tse tšoeu ho fokotsa ho ruruha; E na le oli e khathollang ea citrus joalo ka lavender ho imolla khatello ea maikutlo le lamunu kapa morara ho fokotsa mokhathala.

Ke mang ea fumanang sickle cell anemia?

Mathata a sickle cell anemia ke afe?

sickle cell anemiaE baka mathata a tebileng a hlahang ha lisele tsa sekele li koala methapo ea mali likarolong tse fapaneng tsa 'mele. Lithibelo tse bohloko kapa tse senyang maqakabetsi a sickle cell E bitsoa.

Tse latelang ke tsena sickle cell anemiaMaemo a ka hlahang:

  • khaello ea mali e matla
  • lefu la maoto a letsoho
  • phokotso ya spleen
  • Khōlo e liehang
  • Mathata a methapo ea kutlo joalo ka ho tsietsana le stroke
  • mathata a mahlo
  • liso tsa letlalo
  • Lefu la pelo le lefu la sefuba
  • lefu la matšoafo
  • Priapism
  • nyooko
  • lefu la sefuba sa sekele

Pheko ea tlhaho ea sickle cell anemia

Batho ba nang le sickle cell anemiahape ba na le kotsi e kholo ea ho tšoaroa ke mafu le mafu. Ke habohlokoa hore batho bana ba lule hole le batho ba kulang. Ho hlapa matsoho khafetsa, ho qoba mocheso o feteletseng le serame, ho se ikoetlise ka matla, ho robala ka ho lekaneng le ho noa metsi a lekaneng ke lintlha tse lokelang ho nahanoa.

Haeba matšoao a latelang a hlaha (haholo-holo baneng), batla keletso ea bongaka hang-hang:

  • feberu e fetang 38.5 ° C
  • Ho hema ka thata le bohloko sefubeng le mpeng
  • Hlooho e matla haholo, pono e fetoha, le bothata ba ho tsepamisa mohopolo
  • Hlokomela
Arolelana poso!!!

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